A case report of primary ovarian fibrosarcoma

A case report of primary ovarian fibrosarcoma

Paige Grenier, BSc, MD;1 Anita Agrawal, MSc, MD, FRCSC;1 Rajni Chibbar, PhD, MD, FRCPC2

1Department of Obstetrics and Gynecology, University of Saskatchewan, Saskatoon, SK
2Department of Pathology and Laboratory Medicine, University of Saskatchewan, Saskatoon, SK

International-Journal-of-Case-Reports-2d code

Background: Ovarian fibrosarcoma is a rare malignant tumor that should be distinguished from benign fibrous ovarian tumors and other malignancies, as it has a predilection for early and aggressive metastasis.
Case: A 52-year-old woman presented with a large adnexal mass comprised of atypical spindle cells with increased mitotic activity, high Ki-67 index, and positive vimentin staining, consistent with primary ovarian fibrosarcoma. The patient required multiple laparotomies for large volumes of recurrent, rapidly growing disease. She died 15 months after initial surgery.
Conclusion: Ovarian fibrosarcoma is an important diagnostic consideration when evaluating adnexal masses. Further study is required to clarify the impact of potential prognostic factors and establish optimal management and treatment.

Keywords: Ovarian fibrosarcoma, ovarian tumor, pelvic pain

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How to cite this article:
Paige Grenier, Anita Agrawal, and Rajni Chibbar. A case report of primary ovarian fibrosarcoma. International Journal of Case Reports, 2017 1:10. DOI: 10.28933/ijcr-2017-11-2001.


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