Case Report of International Journal of Case Reports
An unusual Cause of upper airway obstruction in newborn: Congenital nasal pyriform aperture stenosis
Omar Iziki*, Sami Rouadi, Redallah larbi Abada, Mohamed Roubal, Mohamed Mahtar
Department of Otorhinolaryngology, Head and Neck Surgery, King Hassan II University and Ibn Rochd Hospital, Morocco
Congenital nasal pyriform aperture stenosis (CNAPS) is a rare cause of pediatric nasal airway obstruction that clinically mimics choanal atresia in a neonate. CNPAS is suspected clinically and confirmed with CT scanning. Early diagnosis and management is essential for this potentially life-threatening condition. Because of the association this anomaly has with other midline defects, such as holoprosencephaly, it is important to recognize it and pursue a thorough workup. Patients can be managed conservatively or surgically. Surgical treatment is usually reserved for those patients that fail conservative treatment. We present a case of CNPAS, to highlight the importance of recognizing the classic signs of CNPAS on cross-sectional imaging to prevent fatal outcome.
Keywords: Nasal obstruction, pyriform aperture stenosis, congenital, megaincisor.
How to cite this article:
Omar Iziki, Sami Rouadi, Redallah larbi Abada, Mohamed Roubal, Mohamed Mahtar.An unusual Cause of upper airway obstruction in newborn: Congenital nasal pyriform aperture stenosis. International Journal of Case Reports, 2019 4: 77. DOI: 10.28933/ijcr-2019-02-2205 (This article has been withdrawn from International Journal of Case Reports. Please do not use it for any purpose)
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