Isolated temporal bone’s Paget disease: A case report

Isolated temporal bone’s Paget disease: A case report.

Bouzbouz Anas, Abdulhakeem Bushra, Lekhbal Adil, Laababsi Rabii, Rouadi Sami, Abada Reda, Roubal Mohamed, Mahtar.
Department of Otolaryngology Head Neck Surgery, University hospital Ibn Rochd, Casablanca, Morocco.

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Paget’s bone disease (PBD) is a benign tumor of osteoclasts. We report a case of an isolated temporal bone’s Paget disease with unusual evolution to a rapidly functional degradation of vestibulocochlear system.
A 60 years old female was admitted for an isolated, left sided mastoid tumefaction without any inflammatory signs. Initial temporal bone computed tomography (CT) showed a left cotton wool appearance without any ossicles lesion or vestibulocochlear extension. Anatomo pathological tests confirmed the diagnosis. The outcome was marked by the occurrence of vestibulocochlear symptoms. Treatment had consisted on subtotal surgery in combination with oral bisphosphonate with improvement of her clinical conditions. The post operative’s follow-up was simple without any abnormalities
PBD of temporal bone is a benign disorder. Imaging is considered the most useful diagnosis modality for revealing the disorder that will be confirmed by histological tests. The treatment is based on medical approaches and surgery has few indications.

Keywords: Paget disease, bone, hearing loss, temporal bone CT, bisphosphonate.

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Bouzbouz Anas, Abdulhakeem Bushra, Lekhbal Adil, Laababsi Rabii, Rouadi Sami, Abada Reda, Roubal Mohamed, Mahtar.Isolated temporal bone’s Paget disease: A case report.. International Journal of Case Reports, 2019 4:76. DOI: 10.28933/ijcr-2019-03-2805 (This article has been withdrawn from International Journal of Case Reports. Please do not use it for any purpose)


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