Thoracic mediastinal Chordoma an atypical location – Mimicking as Adenocarcinoma


Thoracic mediastinal Chordoma an atypical location – Mimicking as Adenocarcinoma


Sam Supreeth, Sang-Il Kim, Woong-Ki Jeon, Hyung-Youl Park, Ji Hoon Bahk, Chan Kwon Jung, Seok-Hwan Moon, Young-Hoon Kim

1Department of Orthopaedic surgery, Khoula Hospital, Muscat, Oman 2Department of Orthopaedic Surgery, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, Seoul, Korea 3Department of Orthopaedic Surgery, Eunpyeong St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, Seoul, Korea 4Department of Hospital Pathology, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, Seoul, Korea 5Department of Thoracic Surgery, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, Seoul, Korea


International-Journal-of-Case-Reports-2d code

Background: Chordoma, a rare tumor accounting for less than 4% of primary bone tumors of which incidence of thoracic chordoma is 2-5%. Describing an incidental diagnosis of chordoma in a posterior mediastinal mass.
Case description: An asymptomatic 52year lady with an incidental posterior mediastinal mass was diagnosed Adenocarcinoma on endoscopic biopsy of the oesophagus. Nonresponsiveness to chemoradiotherapy warranted en-bloc resection with VATS- assisted thoracotomy which turned to be a Chordoma.
Conclusion: We report this atypical presentation of chordoma mimicking as adenocarcinoma with literature review — a unique learning experience.


Keywords: Thoracic mediastinal Chordoma, atypical location, Mimicking as Adenocarcinoma


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How to cite this article:

Sam Supreeth, Sang-Il Kim, Woong-Ki Jeon, Hyung-Youl Park, Ji Hoon Bahk, Chan Kwon Jung, Seok-Hwan Moon, Young-Hoon Kim. Thoracic mediastinal Chordoma an atypical location – Mimicking as Adenocarcinoma. International Journal of Case Reports, 2020 4:117. DOI: 10.28933/ijcr-2019-12-2105


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