Guilherme Rodrigues Wanderley de Oliveira1* Amanda Thalya Soares da Silva¹, Larissa Jennifer Nascimento Andrade¹, Julliana Carvalho Rocha2, Héberte de Santana Arruda3
1Graduandos em Odontologia pela Universidade Federal de Pernambuco
2Graduanda em Ciências Biológicas Bach pela Universidade Federal de Pernambuco
3Mestrando do programa de pós-graduação em Dentística/Endodontia pela FOP/UPE

American Journal of Anatomy and Physiology 2D

Introduction: To review several studies and reports regarding the causes, diagnoses and characteristics of the study and development of Hutchinson-Gilford Syndrome (HGPS) or progéria.

Methodology: Through articles found in the following databases: PubMed Central, Scielo, BVS, Bireme, Scientific Electronic Library Online.

Discussion: The approach follows from its genetic origin to its progressive stage of incurable aging along with Therapeutic Strategies for greater well-being and longevity for the patient, in the search to minimize the various pathologies that are submitted throughout their life, trying to increase their expectation average of 13.6 years.

Conclusion: Because it is a rare and incurable disease, only palliative treatments for this syndrome are found.

Keywords: Hutchinson, Gilford, Progeria

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Guilherme Rodrigues Wanderley de Oliveira, Amanda Thalya Soares da Silva, Larissa Jennifer Nascimento Andrade, Julliana Carvalho Rocha, Héberte de Santana Arruda.HUTCHINSON-GILFORD SYNDROME: A LITERATURE REVIEW. American Journal of Anatomy and Physiology, 2020, 3:11. DOI:10.28933/ajap-2020-07-2205


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