Sclerosing angiomatoid nodular transformation of the spleen: an unusual cause of abdominal pain


Sclerosing angiomatoid nodular transformation of the spleen: an unusual cause of abdominal pain


Hussien Aly Touny, Einas Al Kuwari, Ahmed Al Moudaris, Salahddin Gehani

Hamad Medical Corporation, Doha, Qatar


International-Journal-of-Case-Reports-2d code

Vascular neoplasms are the most common primary nonhematopoietic tumors of the spleen. They include hemangiomas, littoral cell angiomas, splenic hamartomas, lymphangiomas, hemangioendotheliomas, angiosarcomas, and Sclerosing Angiomatoid Nodular Transformation (SANT)1. SANT is a rare and benign lesion arising from the red pulp of the spleen 2.Martel et al first described the disease entity in 2004 in middle aged- adults with slight female preponderance , the etiology and pathogenesis are still not clear3, SANT poses diagnostic clinical and radiological challenges4, we present this case report with review of the literature.


Keywords: Sclerosing angiomatoid nodular transformation,  spleen, cause of abdominal pain


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How to cite this article:

Hussien Aly Touny, Einas Al Kuwari, Ahmed Al Moudaris, Salahddin Gehani. Sclerosing angiomatoid nodular transformation of the spleen: an unusual cause of abdominal pain. International Journal of Case Reports, 2020 4:141. DOI: 10.28933/ijcr-2020-06-0305


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