Case Report of International Journal of Case Reports
A rare case of Pleuroparenchymal fibroelastosis in Sri Lanka
Prasanjanie A. Jayasinghe, Ruwanthi Jayasekara, Amitha Fernando
National Hospital of Srilanka.
Pleuroparenchymal fibroelastosis (PPFE) is a very rare interstitial lung disease which carries many challenges in the process of diagnosis. A 73 years old female was evaluated for exertional dyspnea with CXR PA evidence of bilateral upper lobe fibrosis and pleural thickening. HRCT revealed typical features suggestive of PPFE. Lung biopsy was not performed considering the risk. Though it is rare PPFE should be considered when evaluating bilateral apical fibrosis. Proper radiological evaluation is paramount important in the process of diagnostic evaluation. Performance of lung biopsy as an essential criterion should be reconsider with associated risks.
Keywords: Pleuroparenchymal fibroelastosis, Sri Lanka
How to cite this article:
Prasanjanie A. Jayasinghe, Ruwanthi Jayasekara, Amitha Fernando. A rare case of Pleuroparenchymal fibroelastosis in Sri Lanka. International Journal of Case Reports, 2020; 4:151. DOI: 10.28933/ijcr-2020-07-1705
1. PI Jayasekera1,2, DW Denning2, PD Perera1, A Fernando3, S Kudavidanage1; Is fungal disease in Sri Lanka underestimated?A comparison of reported fungal infections with estimated disease burden using global data;Sri Lankan Journal of Infectious Diseases 2015 Vol.5 (2):73-85
2. Bonifazi M, Montero MA, Renzoni E A; Idiopathic Pleuroparenchymal Fibroelastosis; Curr Pulmonol Rep (2017) 6:9–15
3. Mariani F, Gatti B, Rocca A, et al. Pleuroparenchymal fibroelastosis: the prevalence of secondary forms in hematopoietic stem cell and lung transplantation recipients. Diagn Interv Radiol. 2016
4. Reddy TL, Tominaga M,Hansell D M, Thusen J V, Rassl D, Parfrey H,etc Pleuroparenchymal fibroelastosis: a spectrum of histopathological and imaging phenotypes;Eur Respir J 2012; 40: 377–385