ANALYSIS OF THE INCIDENCE OF HAEMOGLOBIN S IN NEWBORNS IN PERNAMBUCO, BRAZIL


ANALYSIS OF THE INCIDENCE OF HAEMOGLOBIN S IN NEWBORNS IN PERNAMBUCO, BRAZIL

Natalice Margareth Teixeira Varela1*, Jéssica Vitória Gadelha de Freitas Batista1, Adriana Magna Costa de Carvalho1, Fabio Rodrigo Barbosa Dutra Nascimento1, Marcos André Cavalcanti Bezerra1.


International journal of Pediatric research and reviews-2d

Objective: To analyse the frequency of haemoglobin variants detected in the neonatal screening program in the state of Pernambuco from January / 2015 to July / 2016.

Methodology: Descriptive study based on data provided by the health secretary of the state of Pernambuco referring to newborns submitted to the Guthrie’s test between 01/01/2015 to 07/31/2016.

Results: During the period included in the study, 162,236 children participated in the neonatal screening program to evaluate haemoglobinopathies through the health department. From these, 5,997 (3.69%) presented some haemoglobin variant, being 5.019 (3.09%) carrying HbS in hetero or homozygous.

Conclusions: It was possible to observe a high incidence of children diagnosed as having haemoglobin variants, especially HbS, showing the importance of performing this test so that all children can be assisted from the beginning of their lives.


Keywords: Hematologic disease, Haemoglobinopathies, sickle cell anemia

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How to cite this article:
Natalice Margareth Teixeira Varela, Jéssica Vitória Gadelha de Freitas Batista, Adriana Magna Costa de Carvalho, Fabio Rodrigo Barbosa Dutra Nascimento, Marcos André Cavalcanti Bezerra. ANALYSIS OF THE INCIDENCE OF HAEMOGLOBIN S IN NEWBORNS IN PERNAMBUCO, BRAZIL. IInternational Journal of Pediatric Research and Reviews, 2019, 2:19.


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